Browsing
     by title


0-9 A B C D E F G H I J K L M N O P Q R S T U V W X Y Z

or enter first few letters:   
OK
Peer Reviewed
See detailSpinocerebellar ataxia type 6: genotype and phenotype in German kindreds.
Schols, L.; Krüger, Rejko UL; Amoiridis, G. et al

in Journal of neurology, neurosurgery, and psychiatry (1998), 64(1), 67-73

OBJECTIVE: Spinocerebellar ataxia type 6 (SCA6) is an autosomal dominant cerebellar ataxia (ADCA) of which the mutation causing the disease has recently been characterised as an expanded CAG trinucleotide ... [more ▼]

OBJECTIVE: Spinocerebellar ataxia type 6 (SCA6) is an autosomal dominant cerebellar ataxia (ADCA) of which the mutation causing the disease has recently been characterised as an expanded CAG trinucleotide repeat in the gene coding for the alpha1A-subunit of the voltage dependent calcium channel. The aim was to further characterise the SCA6 phenotype METHODS: The SCA6 mutation was investigated in 69 German families with ADCA and 61 patients with idiopathic sporadic cerebellar ataxia and the CAG repeat length of the expanded allele was correlated with the disease phenotype. RESULTS: Expanded alleles were found in nine of 69 families as well as in four patients with sporadic disease. Disease onset ranged from 30 to 71 years of age and was significantly later than in other forms of ADCA. Age at onset correlated inversely with repeat length. The SCA6 phenotype comprises predominantly cerebellar signs in concordance with isolated cerebellar atrophy on MRI. Non-cerebellar systems were only mildly affected with external ophthalmoplegia, spasticity, peripheral neuropathy, and parkinsonism. Neither these clinical signs nor progression rate correlated with CAG repeat length. CONCLUSIONS: This study provides the first detailed characterisation of the SCA6 phenotype. Clinical features apart from cerebellar signs were highly variable in patients with SCA6. By comparison with SCA1, SCA2, and SCA3 no clinical or electrophysiological finding was specific for SCA6. Therefore, the molecular defect cannot be predicted from clinical investigations. In Germany, SCA6 accounts for about 13% of families with ADCA. However, up to 30% of SCA6 kindreds may be misdiagnosed clinically as sporadic disease due to late manifestation in apparently healthy parents. Genetic testing is therefore recommended for the SCA6 mutation also in patients with putative sporadic ataxia. [less ▲]

Detailed reference viewed: 218 (0 UL)
Full Text
Peer Reviewed
See detailSpiral Colour Model: Reduction from 3-D to 2-D
Garcia Becerro, Frederic UL; Aouada, Djamila UL; Mirbach, Bruno et al

in International Conference on Acoustics, Speech and Signal Processing (2011)

Detailed reference viewed: 177 (2 UL)
Full Text
Peer Reviewed
See detailSpiral growth and step edge barriers
Redinger, Alex UL; Ricken, Oliver; Kuhn, Philipp et al

in PHYSICAL REVIEW LETTERS (2008), 100(3),

The growth of spiral mounds containing a screw dislocation is compared to the growth of wedding cakes by two-dimensional nucleation. Using phase field simulations and homoepitaxial growth experiments on ... [more ▼]

The growth of spiral mounds containing a screw dislocation is compared to the growth of wedding cakes by two-dimensional nucleation. Using phase field simulations and homoepitaxial growth experiments on the Pt(111) surface we show that both structures attain the same large scale shape when a significant step-edge barrier suppresses interlayer transport. The higher vertical growth rate of the spiral mounds on Pt(111) reflects the different incorporation mechanisms for atoms in the top region and can be formally represented by an enhanced apparent step-edge barrier. [less ▲]

Detailed reference viewed: 99 (2 UL)
Full Text
See detailLa Spirale du déclassement. Essai sur la société des illusions
Chauvel, Louis UL

Book published by Seuil (2016)

Notre civilisation de classe moyenne est à la croisée des chemins. Alors qu'elle définissait le projet des démocraties modernes, elle fait face à des défis majeurs. La recristallisation en masse des ... [more ▼]

Notre civilisation de classe moyenne est à la croisée des chemins. Alors qu'elle définissait le projet des démocraties modernes, elle fait face à des défis majeurs. La recristallisation en masse des inégalités, la mobilité descendante, l'écrasement du pouvoir d'achat des salaires relativement aux prix des biens immobiliers, la paupérisation de cohortes entières de jeunes surdiplômés et la globalisation porteuse d'une montée aux extrêmes de la concurrence forment ensemble une spirale de déclassement aux effets potentiellement dévastateurs. Les inégalités de classes et la fracture des générations se renforcent mutuellement : à raison de la dynamique de repatrimonialisation, les écarts au sein des nouvelles générations sont appelés à se radicaliser. Ce sont autant de phénomènes dissimulés sous le voile du déni, qui risquent de réduire à néant l'ambition de laisser à nos enfants un monde meilleur. À partir de données et de comparaisons internationales inédites, Louis Chauvel récuse ici les illusions qui aggravent nos maux. Car les dénégations qu'on oppose aux difficultés réelles des classes moyennes et populaires, des jeunes et de pans entiers de la société ne font qu'aiguiser les frustrations et un ressentiment général dont la traduction politique s'exacerbe. [less ▲]

Detailed reference viewed: 343 (6 UL)
Full Text
See detailSpiritualitéit am Scoutismus
Weber, Jean-Marie UL

Conference given outside the academic context (2016)

Detailed reference viewed: 56 (0 UL)
Peer Reviewed
See detailSpirometrie
Schulz, André UL

in Wirtz, M. A. (Ed.) Dorsch - Lexikon der Psychologie (2019)

Detailed reference viewed: 54 (0 UL)
Full Text
Peer Reviewed
See detailSplitting Leagues: Promotion and Demotion in Contribution-Based Regrouping Experiments
Neugebauer, Tibor UL

in Experimental Economics (2013), 16(3),

Detailed reference viewed: 125 (6 UL)
Full Text
Peer Reviewed
See detailSplitting theorem for Z_2^n-supermanifolds
Covolo, Tiffany; Grabowski, Janusz; Poncin, Norbert UL

in Journal of Geometry and Physics (2016), 110

Detailed reference viewed: 147 (23 UL)
Full Text
Peer Reviewed
See detailSPN2: Single-Sided Privacy Preserving Nearest Neighbor and its Application to Face Recognition
Aouada, Djamila UL; Khader, Dalia UL

in 11th IEEE International Conference on Advanced Video and Signal-Based Surveillance (AVSS'14) (2014)

We address the privacy concerns that raise when running a nearest neighbor (NN) search on confidential data in a surveillance system composed of a client and a server. The proposed privacy preserving NN ... [more ▼]

We address the privacy concerns that raise when running a nearest neighbor (NN) search on confidential data in a surveillance system composed of a client and a server. The proposed privacy preserving NN search uses Boneh-Goh-Nissim encryption to hide both the query data captured by the client and the database records stored in the server. As opposed to state–of–the–art approaches which rely on a large number of interactions, this encryption enables the client to fully outsource the NN computation to the server; hence, ensuring a single-sided private computation, and resulting in a one–round protocol between the server and the client. We analyze the practical feasibility of this algorithm on a face recognition problem. We formally prove and experimentally show that the resulting system maintains the recognition rate while fully preserving the privacy of both the database and the acquired faces. [less ▲]

Detailed reference viewed: 166 (7 UL)
Peer Reviewed
See detailLa spoliation des biens culturels au Luxembourg. Le Landesmuseum Luxemburg pendant la Deuxième Guerre mondiale
Jungblut, Marie-Paule UL

in Gob, André (Ed.) Des musées au-dessus de tout soupçon (2007)

Detailed reference viewed: 61 (5 UL)
Full Text
Peer Reviewed
See detailSPON: Enabling Resilient Inter-Ledgers Payments with an Intrusion-Tolerant Overlay
Trestioreanu, Lucian Andrei UL; Nita-Rotaru, Cristina; Malhotra, Aanchal et al

Scientific Conference (2021, October 04)

Payment systems are a critical component of everyday life in our society. While in many situations payments are still slow, opaque, siloed, expensive or even fail, users expect them to be fast ... [more ▼]

Payment systems are a critical component of everyday life in our society. While in many situations payments are still slow, opaque, siloed, expensive or even fail, users expect them to be fast, transparent, cheap, reliable and global. Recent technologies such as distributed ledgers create opportunities for near-real-time, cheaper and more transparent payments. However, in order to achieve a global payment system, payments should be possible not only within one ledger, but also across different ledgers and geographies.In this paper we propose Secure Payments with Overlay Networks (SPON), a service that enables global payments across multiple ledgers by combining the transaction exchange provided by the Interledger protocol with an intrusion-tolerant overlay of relay nodes to achieve (1) improved payment latency, (2) fault-tolerance to benign failures such as node failures and network partitions, and (3) resilience to BGP hijacking attacks. We discuss the design goals and present an implementation based on the Interledger protocol and Spines overlay network. We analyze the resilience of SPON and demonstrate through experimental evaluation that it is able to improve payment latency, recover from path outages, withstand network partition attacks, and disseminate payments fairly across multiple ledgers. We also show how SPON can be deployed to make the communication between different ledgers resilient to BGP hijacking attacks. [less ▲]

Detailed reference viewed: 51 (4 UL)
Full Text
See detailThe Spontaneous Exchange of Information between European Judicial Authorities from the Italian Perspective
Simonato, Michele UL

in New Journal of European Criminal Law (2011), 2(2), 220

This article outlines the legal grounds which allow for spontaneous exchange of information at the judicial level within the European Union, clarifying the purposes and modalities of such transmission ... [more ▼]

This article outlines the legal grounds which allow for spontaneous exchange of information at the judicial level within the European Union, clarifying the purposes and modalities of such transmission. Furthermore, it provides an overview of the Italian legal system’s approach towards received information. [less ▲]

Detailed reference viewed: 185 (0 UL)
Full Text
Peer Reviewed
See detailSpontaneous macroscopic carbon nanotube alignment via colloidal suspension in hexagonal columnar lyotropic liquid crystals
Scalia, Giusy; von Bühler, Clemens; Hägele, Constanze et al

in Soft Matter (2008), 4(3), 570-576

The self-assembly of amphiphilic molecules in aqueous solution into lyotropic liquid crystals (LCs), characterised by soft yet long-range ordered nanoscale structures, constitutes a fascinating phenomenon ... [more ▼]

The self-assembly of amphiphilic molecules in aqueous solution into lyotropic liquid crystals (LCs), characterised by soft yet long-range ordered nanoscale structures, constitutes a fascinating phenomenon at the heart of soft matter science which can be employed in a manifold of creative ways. Particularly interesting structures may arise as a result of functionalisation of the LC with appropriate guest molecules, adopting the order of their host. Here we combine cat- and anionic surfactants to form a liquid-crystalline colloidal suspension of carbon nanotubes (CNTs), which by virtue of the spontaneously formed hexagonal columnar LC structure are uniaxially aligned over macroscopic areas. The nanotube concentration can be so high, with sufficiently uniform alignment, that the mixture becomes a fluid linear polariser, the anisotropic optical properties of CNTs having been transferred to macroscopic scale by the LC. Moreover, thin and highly aligned filaments can be drawn and deposited in selected directions on arbitrary surfaces, after which the LC template can be rinsed away. Combined with recently developed methods for CNT fractionation according to chirality, the technique would yield an unprecedented degree of control in the practical realisation of carbon nanotube-based devices and materials. [less ▲]

Detailed reference viewed: 121 (1 UL)
Full Text
Peer Reviewed
See detailSpontaneous Networking with CORBA, Jini & JavaCards in RoamX, a Mobile X-Desktop
Rothkugel, Steffen UL; Sturm, Peter

in DOA '00: Proceedings of the International Symposium on Distributed Objects and Applications (2000)

Detailed reference viewed: 37 (0 UL)
Peer Reviewed
See detailSpontanschreibung
Weth, Constanze UL

in Kilian, Jörg; Rymarczyk, Jutta (Eds.) Language Learning: First Language, Second Language, Foreign Language (2016)

Detailed reference viewed: 87 (5 UL)
See detailSporadic democracy: Education and the question of inclusion.
Biesta, Gert UL

in Katz, M.; Verducci, S.; Biesta, Gert (Eds.) Education,democracy and the moral life (2009)

Detailed reference viewed: 79 (0 UL)
See detailSport and Urban Space in Europe: Facilities, Industries, Identities
Terret, Thierry; Heck, Sandra UL

Book published by Routledge (2016)

Filling a gap in the literature on the history of sport in Europe, the book brings together complementary studies on diverse aspects of the interrelation between sport and urban space. Going from ... [more ▼]

Filling a gap in the literature on the history of sport in Europe, the book brings together complementary studies on diverse aspects of the interrelation between sport and urban space. Going from geography to political science, from sports history to urban and transport history, it suggests a three-fold approach. A first thematic group of researches ranges around "Sport Development and Urban Spaces", exploring the impact of the city on the rise of sport. A second focal point is related to "Sport Policies and Local Identities" with a special attention given to the making of sport venues and competitions in the making of urban identity. A third thematic group includes studies on "Sport Facilities, Engineers and Workers". The articulation of the three parts builds a unique contribution to the process of identity making at a European level. [less ▲]

Detailed reference viewed: 36 (0 UL)
Full Text
See detailSport beginnt und endet im Kopf
Steffgen, Georges UL

Article for general public (1991)

Detailed reference viewed: 18 (1 UL)